erythrokeratodermia variabilis

erythrokeratodermia variabilis
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English-Arabic Medical Dictionary. 2013.

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  • Erythrokeratodermia variabilis — Classification and external resources OMIM 133200 Erythrokeratodermia variabilis (also known as Erythrokeratodermia figurata variabilis, Keratosis extremitatum progrediens, Keratosis palmoplantaris transgrediens et progrediens, [1] …   Wikipedia

  • erythrokeratodermia variabilis — a rare autosomal dominant condition present at birth, characterized by both transient, migratory areas of erythroderma in various shapes and fixed plaques of hyperkeratosis. Called also keratoderma palmoplantare transgrediens and keratosis… …   Medical dictionary

  • erythrokeratodermia — A neurocutaneous syndrome characterized by papulosquamous erythematous plaques with onset shortly after birth; ataxia, nystagmus, dysarthria, and decreased tendon reflexes appear later in life; symmetrical progressive e. is inherited as an …   Medical dictionary

  • EKV — erythrokeratodermia variabilis …   Medical dictionary

  • keratoderma palmoplantare transgrediens — erythrokeratodermia variabilis …   Medical dictionary

  • keratosis palmoplantaris transgrediens — erythrokeratodermia variabilis …   Medical dictionary

  • Mendes da Costa syndrome — erythrokeratodermia variabilis …   Medical dictionary

  • EKV — • erythrokeratodermia variabilis …   Dictionary of medical acronyms & abbreviations

  • GJB3 — Gap junction protein, beta 3, 31kDa, also known as GJB3, is a human gene.cite web | title = Entrez Gene: GJB3 gap junction protein, beta 3, 31kDa| url = http://www.ncbi.nlm.nih.gov/sites/entrez?Db=gene Cmd=ShowDetailView TermToSearch=2707|… …   Wikipedia

  • GJB4 — Gap junction protein, beta 4, also known as GJB4, is a human gene.cite web | title = Entrez Gene: GJB4 gap junction protein, beta 4| url = http://www.ncbi.nlm.nih.gov/sites/entrez?Db=gene Cmd=ShowDetailView TermToSearch=127534| accessdate = ] PBB …   Wikipedia

  • Ichthyosis — Classification and external resources Ichthyosis is recognized by rough, scaly skin exhibited by patients. ICD 10 Q …   Wikipedia

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